IntroductionCongenital agenesis of major salivary glands is a rare entity with unclear etiopathogenesis.1-7 Pleomorphic adenoma arising from an accessory parotid gland is also rare. We report an unusual case of unilateral agenesis of the left parotid gland associated with pleomorphic adenoma of the left accessory parotid gland, demonstrated on computed tomography (CT).



