Lymphangioma is an uncommon benign pathology, usually reported in children and rarely in adults. In the past, the definitive diagnosis was made intraoperatively and was usually an unexpected finding. However, with today's modern imaging technologies, such as computed tomography and magnetic resonance imaging, the diagnosis can be assumed before intervention, even though the final diagnosis still can be reached only via histopathologic examination. Imaging techniques also can aid in the precise mapping of the lesion and in defining its boundaries with the surrounding vital structures, improving therapeutic success. Various therapeutic options are reported in literature, but complete surgical excision is still considered the best approach. We report a case of cervical lymphangioma of unknown etiology in an 18-year-old man and discuss the presentation, diagnosis, and management of this lesion.