Sinonasal type hemangiopericytomas are very rare tumors, and are often called glomangiopericytoma. They are believed to be derived from perivascular modified smooth muscle cells. Their origin is similar to glomus tumors but some distinct differences exist. Glomangiopericytomas are indolent tumors and overall survival rates are higher after complete surgical excision. Recurrence rates are as high as 30%. We present a case of glomangiopericytoma which involves the orbital wall, noteworthy because such bone-dissolving glomangiopericytomas are extremely rare.
Hemangiopericytomas, commonly known as glomangiopericytomas, are very rare. They are thought to derive from modified perivascular smooth muscle cells. Although hemangiopericytomas may occur in almost any part of the body, they are generally restricted to the sinonasal cavities.1